Mucosa-Associated Lymphoid Tissue (MALT) lymphoma is most commonly seen in older adults and has a female predilection. It is rare in children and extremely uncommon in the lip with only three cases reported in the lip of pediatric patients. In those reported cases the MALT lymphoma was isolated to a single lip. We report a case of primary MALT lymphoma in an immunocompetent male pediatric patient involving both the upper and lower lips. To the best of our knowledge, this is the first reported case.